Cardiovascular (CVS)
AA01	Aortic valve stenosis	746300-746309
AA02	Atrial septal defect	745510-745599
AA03	Atrioventricular septal defect (Endocardial cushion defect)	745600-745699 or 745487
AA04	Coarctation of the arota	747100-747199
AA05	Common truncus (truncas arteriosus or TA)	745000-745009
AA06	Double outlet right ventricle (DORV)	745130-745159
AA07	Ebstein anomaly	746200-746209
AA08	Hypoplastic left heart syndrome	746700-746709
AA09	Interrupted aortic arch (IAA)	747215-747217 or 747285
AA10	Pulmonary valve atresia and stenosis	746000-746019
AA11	Single Ventricle	745300-745309
AA12	Tetralogy of Fallot (TOF)/Trilogy of Fallot	745200-745219 or 747310-747319 or 746840-746849
AA13	Total anomalous pulmonary venous connection (TAPVC)	747420-747429
AA14	Transposition of the great arteries (TGA)	745100-745129 or 745180-745199
AA15	Tricuspid valve atresia and stenosis	746100-746104 or 746106
AA16	Ventricular septal defect	745400-745486 or 745489-745499

	Orofacial (ORF)
BB01	Choanal atresia	748000-748009
BB02	Cleft lip with cleft palate	749200-749299
BB03	Cleft lip alone (without cleft palate)	749100-749199
BB04	Cleft palate alone (without cleft lip)	749000-749099

	Eye (EYE)
CC01	Anophthalmia/microphthalmia	743000-743109
CC02	Congenital cataract	743320-743329

	Ear (EAR)
DD01	Anotia/microtia	744010-744019 or 744210-744219

	Gastrointestinal (GSI)
EE01	Biliary atresia	751650-751659
EE02	Esophageal atresia/tracheosophageal fistula	750300-750359
EE03	Rectal and large intestinal atresia/stenosis	751200-751249
EE04	Small intestinal atresia/stenosis	751100-751199

	Central Nervous System (CNS)
FF01	Anencephalus	740000-740109
FF02	Spina bifida without anencephalus	741000-741999 and BPA not equal to 740000-740109
FF03	Encephalocele	742000-742099
FF04	Holoprosencephaly	742260-742269

	Genitourinary (GTU)
GG01	Bladder exstophy	753500-753509
GG02	Congenital posterior urethral valves	753600-753609
GG03	Hypospadias	752600-752609 or 752620 or 752622-752629
GG04	Renal agenesis/hypoplasia	753000-753019

	Musculoskeletal (MSK)
HH01	Clubfoot	754500-754509 or 754730-754734 or 754736-754739
HH02	Craniosynostosis	756000-756039
HH03	Diaphragmatic hernia	756610-756617
HH04	Gastroschisis	756710-756719
HH05	Limb deficiencies (reduction defects)	755200-755499
HH06	Omphalocele	756700-756709

	Chromosomal (CHR)
II01	Deletion 22 q11	758370-758379
II02	Trisomy 13	758100-758199
II03	Trisomy 18	758200-758299
II04	Trisomy 21 (Downs syndrome)	758000-758099
II05	Turner syndrome	758600-758699

Multiple Birth Defects in the Same Child

An infant or fetus can have multiple birth defects. For example, an infant/fetus with a cleft lip and spina bifida is counted when cleft lip is queried and is counted when spina bifida is queried. Therefore the total of the two queries cannot be added to reach a total number of infant/fetuses.

Birth Prevalence (expressed as cases of a birth defect of interest per a standard number of live births)

Ideally, incidence rates would be used instead of prevalence to measure birth defect occurrence. Since the number of conceptions is unknown, as is the number of cases “lost” through spontaneous abortions, technically speaking we cannot determine incidence. Because of this, most individuals working in the area of birth defects use the term ‘birth prevalence’ to refer to birth defect occurrence.

The formula for birth prevalence (expressed as cases of a defect of interest per 10,000 live births):
The number of infants with the birth defect of interest in an area and time period / by the number of live births in that area and time period * 10,000

EXAMPLE: 62 cases of hypoplastic left heart syndrome statewide delivered in 2009-2013 / 266,073 live births in 2009-2013 = 2.33 cases per 10,000 live births

County: (Map of Oklahoma Counties)

The county of residence at the time of the birth defect diagnosis.

Regions: (Map of Regions)

Region	Counties
Central	Cleveland, Oklahoma
Northeast	Adair, Cherokee, Craig, Creek, Delaware, Kay, Lincoln, Mayes, Muskogee, Noble, Nowata, Okfuskee, Okmulgee, Osage, Ottawa, Pawnee, Payne, Rogers, Sequoyah, Wagoner, Washington
Northwest	Alfalfa, Beaver, Blaine, Canadian, Cimarron, Custer, Dewey, Ellis, Garfield, Grant, Harper, Kingfisher, Logan, Major, Roger Mills, Texas, Woods, Woodward
Southeast	Atoka, Bryan, Choctaw, Coal, Haskell, Hughes, Johnston, Latimer, LeFlore, Marshall, McCurtain, McIntosh, Murray, Pittsburg, Pontotoc, Pottawatomie, Pushmataha, Seminole
Southwest	Beckham, Caddo, Carter, Comanche, Cotton, Garvin, Grady, Greer, Harmon, Jackson, Jefferson, Kiowa, Love, McClain, Stephens, Tillman, Washita
Tulsa	Tulsa

Race

The race categories used by the OBDR are: White/Caucasian, Black/African American, American Indian/Alaskan Indian, Asian/Pacific Islander, Other/Unknown, and Hispanic.